Congenital heart disease (CHD) is one of the most common birth defects, with an incidence of nine out of every 1,000 live births. Critical CHD (CCHD) is defined as cardiac lesions that require surgery or cardiac catheterization within the first month (or within the first year by different definitions) of life to prevent death or severe end-organ damage. An early diagnosis and timely intervention can significantly reduce the likelihood of an adverse outcome. However, studies from the United States and other developed countries have shown that as many as 30%–50% of infants with CCHD are discharged after birth without being identified. Pulse oximetry is a tool to measure oxygen saturation, and based on the presence of hypoxemia, many cardiac lesions are detected. Due to its ease of application to the patient, providing results in a timely manner and without the need for calibrating the sensor probe, pulse oximetry offers many advantages as a screening tool. Pulse oximetry was recommended as a screening tool to detect critical CHD in 2011 by the American Academy of Pediatrics and the American Heart Association. Pulse oxymetry screening (POS) for early detection of CCHD is a simple, noninvasive, and inexpensive test, which meets the necessary criteria for inclusion to universal newborn screening panel. Wider acceptance and adoption can significantly decrease morbidity and mortality in infants with CCHD.

Congenital heart disease is the most common group of congenital disorder with a reported prevalence that rates from 8/1000 live births. Also, CHD accounts for nearly one-third of all major congenital anomalies. In recent years, the country’s congenital heart disorders diagnosis has improved significantly, but has been of late diagnosis of cases.Once the diagnosis of congenital heart disorders later case, the resultant complications occurred because the majority is unable to similarly cardiac surgical treatment. Therefore, early diagnosis of congenital heart defects, and thus treatment is necessary to solve the problem early.A retrospective, descriptive study was conducted from January 1st8 2012 and January 1st8 2013 there were 263 deliveries at the Urgoo maternal hospital and child health research center of Mongolia. We reviewed the medical records of all neonatal in 2012-2013 who were born in the Urgoo maternity hospital of Ulaanbaatar and NICU and NCU of National Center of Maternal and Child Health. A total of 263 infants with congenital heart disease.The number of neonatal intensive care unit and neonatal unit with Congenital heart defect was 99 (37.7%) in 2012 were as there 164 (62.3%) in 2013 increasing 1.4 times respectively. A total of 263 infants met the inclusion criteria, of whom 130 (55.1%) were males. The reasons for the higher incidence of congenital heart defect observed in infants remain unclear.The most frequently occurring conditions were patent ductus arteriosus /21.7%/, arterial septal defect with patent foramen ovale /41.2%/, other majority defect-31.9%, Dextracaria-5,2%. This raises question regarding the clinical significance of some of lesions, such as small VSDs, which are widely considered to be congenital heart defects. When all clinical presentations of heart disease were analyzed together, atrial septal defect (ASD), Ventricular septal defect (VSD), and Patent ductus arteriosus (PDA) accounted for 62.9% of all defects identified. From diagnosed CHD with percent less than was critical congenital heart defect, which required urgent surgical treatment in neonate period.CHD is expected to increase in the coming years. Thus, when the fetus is affected by a malignant diagnosis.According to the survey findings to diagnose congenital heart defects in the first weeks of the prognosis and treatment options, and shows that it is important to prevent complications. Obstetric and regional diagnostic centers in rural pediatric cardiologist and ultrasound machines shows that it is important for diagnosis and treatment.