A 22 year old nulligravid presented with progressively increasing dysmenorrhea. Transvaginal ultrasound showed a unicornuate uterus with a functioning left rudimentary horn which was confirmed on exploratory laparotomy. The patient was also found to have a missing right fallopian tube and ovary. Excision of the left rudimentary horn was done. The surgery resulted in the patient with a remaining hemiuterus on one side and a separate fallopian tube with the ovary on the other. A very limited number of case reports are available in the literature to describe concomitant occurrence of gonadal and uterine developmental abnormalities. Rarer still is the occurrence of a unilateral fallopian tube and ovary contralateral to a unicornuate uterus. Its possible pathogenesis and implications on the patient's reproductive outlook are discussed.
		                        		
		                        		
		                        		
		                        			Human
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		                        			 Female
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		                        			 Young Adult
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		                        			 ABNORMALITIES
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		                        			 UTERUS