Interstitial lung disease associated with juvenile dermatomyositis
10.3760/cma.j.issn.1673-4408.2020.10.008
- VernacularTitle:幼年皮肌炎相关间质性肺病研究进展
- Author:
Juan LIAO
1
;
Donghong PENG
Author Information
1. 重庆医科大学附属儿童医院呼吸科，儿童发育疾病研究教育部重点实验室，国家儿童健康与疾病临床医学研究中心，儿童发育重大疾病国家国际科技合作基地，儿科学重庆市重点实验室 400010
- From:
International Journal of Pediatrics
2020;47(10):708-712
- CountryChina
- Language:Chinese
-
Abstract:
Juvenile dermatomyositis is a systemic autoimmune vascular disease characterized by rash and proximal myopathy.Pulmonary complications related to this disease include interstitial lung disease, aspiration pneumonia, respiratory muscle involvement, airway involvement, pleural involvement, pulmonary hypertension and mediastinal emphysema .Interstitial lung disease is the most common pulmonary involvement in juvenile dermatomyositis, which often affects the prognosis of children.Adult myositis associated interstitial lung disease has been well described in the literature, but the description of juvenile dermatomyositis associated interstitial lung disease is still lacking.This review discusses the pathogenesis, pathological types, biological markers, diagnosis, treatment and monitoring of juvenile dermatomyositis related interstitial lung disease.
