A Case of Langerhans Cell Sarcoma Presenting as Submandibular Gland Mass
10.3342/kjorl-hns.2018.00661
- Author:
Geonho LEE
1
;
Kunho SONG
;
Ki Wan PARK
;
Bon Seok KOO
Author Information
1. Department of Otorhinolaryngology-Head and Neck Surgery, School of Medicine, Chungnam National University, Daejeon, Korea. bskoo515@cnuh.co.kr
- Publication Type:Case Report
- From:Korean Journal of Otolaryngology - Head and Neck Surgery
2019;62(9):520-523
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Langerhans cell sarcoma is a rare, proliferative tumor of Langerhans cells, which shows cytologic characteristics and clinical features of malignant tumor. Langerhans cell sarcoma primarily occurs in lymph nodes, skin, lung, liver, and spleen. However, very few cases have been reported in the head and neck region. Because of its rarity, an optimal treatment approach is unknown; however, Langerhans cell sarcoma grows aggressively and shows a poor prognosis, such that a more aggressive and multi-modality treatment approach is necessary. Here, we report the case of a 36-year-old male with Langerhans cell sarcoma, who presented with a mass in the submandibular gland area and was treated with wide excision and postoperative radiotherapy.
