Hughes-Stovin Syndrome as an Outcome of Behçet Disease or as a Different Entity
10.5090/kjtcs.2018.51.1.64
- Author:
Serkan DEMIRKAN
1
;
Yıldırım GÜLTEKIN
Author Information
1. Department of Dermatology and Venerology, Kirikkale University Faculty of Medicine, Turkey. serkan.demirkan@yahoo.com.tr
- Publication Type:Case Report
- Keywords:
Hughes-Stovin syndrome;
Behçet disease;
Pulmonary artery aneurysms;
Thrombosis;
Oral ulcer
- MeSH:
Aneurysm;
Behcet Syndrome;
Eponyms;
Hemoptysis;
Humans;
Lower Extremity;
Oral Ulcer;
Pulmonary Artery;
Thrombophlebitis;
Thrombosis;
Venous Thrombosis
- From:The Korean Journal of Thoracic and Cardiovascular Surgery
2018;51(1):64-68
- CountryRepublic of Korea
- Language:English
-
Abstract:
Hughes-Stovin syndrome is a rare disorder of unknown etiology. Although the association between multiple pulmonary artery aneurysms and venous thrombosis of the lower limbs was reported by Beattie and Hall in 1911, it was not until 1962 that the eponym “Hughes-Stovin syndrome” was formally introduced in the medical literature. We describe 2 patients with Hughes-Stovin syndrome who presented with pulmonary artery aneurysm, thrombophlebitis, hemoptysis, and oral ulcers, review the manifestations of the disease, and compare its similarities with and differences from Behçet disease.
