Congenital Esophageal Stenosis in Children: From Etiology to Prognosis
10.13029/jkaps.2018.24.1.1
- Author:
Soo Hong KIM
1
;
Hyun Young KIM
Author Information
1. Department of Pediatric Surgery, Pusan National University Children's Hospital, Yangsan, Korea.
- Publication Type:Review
- Keywords:
Congenital esophageal stenosis;
Esophagus;
Tracheobronchial remnants;
Child
- MeSH:
Child;
Deglutition Disorders;
Diagnosis;
Diaphragm;
Dilatation;
Endosonography;
Esophageal Stenosis;
Esophagus;
Humans;
Hypertrophy;
Mass Screening;
Parturition;
Prognosis;
Rare Diseases;
Vomiting;
Weaning
- From:Journal of the Korean Association of Pediatric Surgeons
2018;24(1):1-4
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Congenital esophageal stenosis (CES) is a rare disease that has been reported to occur once in every 25,000 to 50,000 births. According to its etiology, CES is divided into 3 subtypes, tracheobronchial remnants (TBR), fibromuscular hypertrophy (FMH) and membranous diaphragm (MD). Symptoms begin at the weaning period and the introduction of solid food around 6 months with dysphagia and vomiting. Esophagography is first screening test and endoscopic ultrasonography plays important roles to diagnose subtypes deciding therapeutic plan. TBRs were generally treated with surgical resection and end-to-end anasotomosis, whereas FMH and MD had good response rate to endoscopic or radiologic guided dilatation. This article reviews the literature on the etiology, clinical course, diagnosis and management of CES including recent opinion.
