Management of Coronary Sinus Ostial Atresia during a Staged Operation of a Functional Single Ventricle.
10.5090/kjtcs.2018.51.2.130
- Author:
Seung Ri KANG
1
;
Won Kyoun PARK
;
Bo Sang KWON
;
Jae Kon KO
;
Hyun Woo GOO
;
Jeong Jun PARK
Author Information
1. Division of Pediatric Cardiac Surgery, Asan Medical Center, University of Ulsan College of Medicine, Korea.
- Publication Type:Case Report
- Keywords:
Coronary sinus;
Fontan procedure;
Heart bypass, right
- MeSH:
Coronary Sinus*;
Drainage;
Fontan Procedure;
Heart;
Heart Bypass, Right;
Humans;
Vena Cava, Superior
- From:The Korean Journal of Thoracic and Cardiovascular Surgery
2018;51(2):130-132
- CountryRepublic of Korea
- Language:English
-
Abstract:
Coronary sinus ostial atresia (CSOA) with persistent left superior vena cava (LSVC) in the absence of an unroofed coronary sinus is a benign and rare anomaly that may be taken lightly in most instances. However, if overlooked in patients undergoing univentricular heart repair such as bidirectional Glenn or Fontan-type surgery, fatal surgical outcomes may occur due to coronary venous drainage failure. We report a case of CSOA with a persistent LSVC that was managed through coronary sinus rerouting during a total cavopulmonary connection, and provide a review of the literature regarding this rare anomaly.
