Open Heart Surgery Using a Centrifugal Pump in a Patient Suffering from Hereditary Spherocytosis.
10.4326/jjcvs.23.280
- VernacularTitle:遺伝性球状赤血球症を合併した心房中隔欠損症に対する遠心ポンプを用いた開心術の経験
- Author:
Yohichi Hara
;
Shingo Ishiguro
;
Hiroaki Kuroda
;
Tohru Mori
- Publication Type:Journal Article
- From:Japanese Journal of Cardiovascular Surgery
1994;23(4):280-283
- CountryJapan
- Language:Japanese
-
Abstract:
A very rare case of open heart surgery associated with hereditary spherocytosis (HS) is reported. A 10-year-old girl was admitted for repair of an atrial septal defect (ASD). She was found to have HS by the microscopic findings of a blood smear and characteristic osmotic fragility, but splenectomy had not been undertaken preoperatively. She underwent successful radical operation by means of a centrifugal pump, and poloxamer 188 and haptoglobin were used during cardiopulmonary bypass for prevention of hemolysis. No significant hemolysis occurred intra- or postoperatively. Cardioplumonary bypass using a centrifugal pump appeared to be effective in this patient with HS.
