A Case of Emergency Surgery for a Huge Primary Right Atrial Angiosarcoma with Right Ventricular Failure and Shock
10.4326/jjcvs.40.322
- VernacularTitle:右心不全によるショックにて緊急手術を行った巨大右房原発血管肉腫の1例
- Author:
Yuji Kato
;
Masanori Kato
;
Mitsuhisa Kotani
;
Kazuhiro Hisamoto
;
Yukiharu Sugimura
;
Masaaki Toyama
- Publication Type:Journal Article
- Keywords:
primary cardiac tumor;
angiosarcoma;
right heart failure
- From:Japanese Journal of Cardiovascular Surgery
2011;40(6):322-325
- CountryJapan
- Language:Japanese
-
Abstract:
We encountered a rare case of a 75-year-old woman who fell into right ventricular failure and shock with a comparatively rapid course due to a huge primary right atrial angiosarcoma occupying the right atrium. An emergency surgical excision of the tumor was performed and the right atrium was reconstructed with an EPTFE patch under cardiopulmonary bypass. On account of the positive margin, postoperative radiotherapy was added. There was no local recurrence, but adjuvant chemotherapy was performed for multiple lung and liver metastases 14 months after surgery. Primary cardiac angiosarcomas are extremely rare and have dismal prognoses. Although a complete surgical resection is the cornerstone of treatment, multidisciplinary therapy may improve patient outcomes.
