Mazabraud's Syndrome Coexisting with a Uterine Tumor Resembling an Ovarian Sex Cord Tumor (UTROSCT): a Case Report.
	    		
		   		
		   			
		   		
	    	
    	- Author:
	        		
		        		
		        		
			        		Cuneyt CALISIR
			        		
			        		
			        		
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			        		Ulukan INAN
			        		
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			        		Ulas Savas YAVAS
			        		
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			        		Serap ISIKSOY
			        		
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			        		Tamer KAYA
			        		
			        		
		        		
		        		
		        		
			        		
			        		Author Information
			        		
 - Publication Type:Case Report
 - Keywords: Fibrous dysplasia; Monostotic; Myxoma; Uterine neoplasms
 - MeSH: Aged; Biopsy; Buttocks/pathology/surgery/ultrasonography; Diagnosis, Differential; Female; Fibrous Dysplasia, Monostotic/complications/*diagnosis/surgery; Humans; Magnetic Resonance Imaging; Myxoma/complications/*diagnosis/surgery; Ovarian Neoplasms/*diagnosis; Rare Diseases; Sex Cord-Gonadal Stromal Tumors/*diagnosis; Syndrome; Uterine Neoplasms/complications/*diagnosis/surgery
 - From:Korean Journal of Radiology 2007;8(5):438-442
 - CountryRepublic of Korea
 - Language:English
 - Abstract: The association of intramuscular myxoma and fibrous dysplasia is a rare disease known as Mazabraud's syndrome. We present a case of Mazabraud's syndrome coexisting with a uterine tumor and resembling an ovarian sex cord tumor (UTROSCT). This uterine tumor showed a high mitotic index and cytological atypia. To the best of our knowledge, the coexistence of the two different entities has not been reported in the literature.
 
            