Anatomical Variations, Genitourinary Anomalies and Clinical Presentations in Obstructed Hemivagina and Ipsilateral Renal Anomaly Syndrome: Case Series
- Author:
Hyun Jeong KIM
1
;
Eun Ji LEE
;
Yun-Woo CHANG
;
Seong Sook HONG
;
Jiyoung HWANG
;
Boda NAM
;
Sung Hwan BAE
Author Information
- Publication Type:Case Series
- From: Journal of the Korean Society of Radiology 2025;86(1):129-140
- CountryRepublic of Korea
- Language:English
- Abstract: Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome is a rare Müllerian duct anomaly, commonly characterized by uterus didelphys, obstructed hemivagina, and ipsilateral renal agenesis. While these are the three most common genitourinary anomalies in OHVIRA syndrome, a spectrum of urogenital anomalies can be present. Knowledge of this spectrum is crucial for proper patient management and treatment planning. In this case series, we report on five patients with OHVIRA syndrome, each presenting with a urogenital anomaly other than the typical renal agenesis or uterus didelphys. We highlight the gynecological complications encountered, which clinicians and radiologists should be aware of.
