A Case of Pachydermoperiostosis Combined with Undifferentiated Arthritis.
10.4078/jrd.2015.22.4.256
- Author:
Jung Hoon LEE
1
;
Seung Pyo HONG
;
Jun Kwon KO
;
Eun Young LEE
;
Kang Lok LEE
;
Sung Jun CHUNG
;
Gun Woo KOO
;
So Young BANG
;
Hye Soon LEE
Author Information
1. Department of Internal Medicine, Hanyang University College of Medicine, Seoul, Korea. lhsberon@hanyang.ac.kr
- Publication Type:Case Report
- Keywords:
Pachydermoperiostosis;
Primary hypertrophic osteoarthropathy;
Undifferentiated arthritis
- MeSH:
Arthritis*;
Forehead;
Humans;
Hyperhidrosis;
Knee;
Osteoarthropathy, Primary Hypertrophic*;
Periostitis;
Rare Diseases;
Scalp
- From:Journal of Rheumatic Diseases
2015;22(4):256-259
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Pachydermoperiostosis (PDP) is a primary hypertrophic osteoarthropathy characterized by digital clubbing, pachydermia, and periostosis, which is inherited as an autosomal dominant or recessive trait. We report on a patient suffering from bilateral knee arthritis for 6 years who was newly diagnosed as PDP. PDP was confirmed by bilateral digital clubbing, hyperhidrosis, and cutis verticis gyrata, findings of pachydermatosis on the forehead and scalp, X-ray findings of proliferative periostitis. This case indicates that PDP is one of several possible rare diseases that should be considered in patients with undifferentiated arthritis.
