Recent advance in primary central nervous system vasculitis with spinal cord involvement
10.3760/cma.j.cn115354-20230708-00380
- VernacularTitle:脊髓受累原发性中枢神经系统血管炎的临床研究进展
- Author:
Li ZHANG
1
;
Hui SUN
;
Shimin ZHANG
;
Sai GAO
;
Lei WU
;
Dehui HUANG
Author Information
1. 解放军总医院第一医学中心神经内科医学部,北京 100853
- Keywords:
Primary angiitis of the central nervous system;
Spinal cord involvement;
Magnetic resonance imaging;
Electromyography
- From:
Chinese Journal of Neuromedicine
2023;22(9):960-964
- CountryChina
- Language:Chinese
-
Abstract:
Primary angiitis of the central nervous system (PACNS) is a rare autoimmune disease of the central nervous system, and spinal cord involvement is a rare subtype. The imaging findings of this subtype lack specificity; it is easily misdiagnosed, missed diagnosed, enjoying high disease recurrence rate, disability and mortality. Therefore, this article reviews the clinical manifestations, diagnoses and treatments of PACNS patients with spinal cord involvement, in order to increase clinicians' understanding of the disease.