Spontaneously Regressed Immunoglobulin IgG4-related Lung Disease Presenting as Multiple Cavitary Nodules.
10.3904/kjm.2016.90.5.449
- Author:
Young Jun PARK
1
;
Tae Wook YOON
;
Geun Yong JUNG
;
Ji Hwan CHUNG
;
Joon Young CHOI
;
Eun Joo KIM
;
Hyo Jeong LIM
Author Information
1. Department of Internal Medicine, Veterans Health Service Medical Center, Seoul, Korea. lregulus38@gmail.com
- Publication Type:Case Report
- Keywords:
Immunoglobulin G;
Multiple pulmonary nodules;
Corticosteroids
- MeSH:
Adrenal Cortex Hormones;
Fibrosis;
Immunoglobulin G;
Immunoglobulins*;
Lung Diseases*;
Lung Diseases, Interstitial;
Lung*;
Multiple Pulmonary Nodules;
Phlebitis;
Steroids
- From:Korean Journal of Medicine
2016;90(5):449-454
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Immunoglobulin (Ig) G4-related disease was recently recognized as a systemic fibro-inflammatory disease characterized by dense lymphoplasmacytic infiltrates, storiform fibrosis, and obliterative phlebitis with IgG4-positive cells in the target tissues. This disease can localize to a single organ or be diffuse in multiple organs. Pulmonary manifestation in IgG4-related lung disease presents as various sized nodules, lung masses, patchy ground-glass opacities, consolidation, thickened bronchovascular bundles, nodular pleural lesions, and interstitial lung disease. Traditional treatment for IgG4-related lung disease includes systemic (cortico) steroids. Here, we report a case of IgG4-related lung disease presenting as multiple cavitary nodules that spontaneously regressed without systemic steroid use.