Chronic Thromboembolic Pulmonary Hypertension and ChronicThromboembolic Pulmonary Disease
10.12376/j.issn.2097-0501.2023.01.003
- VernacularTitle:慢性血栓栓塞性肺动脉高压和慢性血栓栓塞性肺疾病
- Author:
Shenshen HUANG
1
;
Jiayong QIU
2
;
Yimin MAO
1
Author Information
1. Department of Respiratory and Critical Care Medicine, the First Affiliated Hospital of Henan University of Science and Technology, Luoyang 471000, China.
2. Department of Respiratory and Critical Care Medicine, the First Affiliated Hospital of Henan University of Science and Technology, Luoyang 471000, China.Department of Respiratory and Critical Care Medicine, the Second Hospital of Hebei Medical University, Shijiazhuang 050000, China.
- Publication Type:Journal Article
- Keywords:
chronic thromboembolic pulmonary hypertension;
chronic thromboembolic pulmonary disease;
pulmonary thromboembolism
- From:
JOURNAL OF RARE DISEASES
2023;2(1):17-26
- CountryChina
- Language:Chinese
-
Abstract:
Chronic thromboembolic pulmonary hypertension (CTEPH) and chronic thromboembolic pulmonary disease (CTEPD) are diseases that occur after acute pulmonary embolism resulting from residual and organized intra-pulmonary thrombus, with or without pulmonary hypertension(PH). The prognosis of these diseases has been dramatically improved with the continuous progress of treatment and the updated concept of the comprehensive treatment strategy. However, there is a lack of awareness of these diseases among medical practitioners, and a lack of epidemiological data in China, with unknown pathogenesis and non-specific clinical manifestations. Therefore, it is easy to misdiagnosis, underdiagnosis and delay diagnosis in clinical practice. To enhance the understanding of medical personnel, this paper summarizes the definition, epidemiology, pathology, pathogenesis, diagnosis and treatment of CTEPH and CTEPD.