Berry syndrome is an extremely rare congenital cardiac anomaly characterized by a combination of aortopulmonary window, aortic origin of the right pulmonary artery, interrupted or hypoplastic aortic arch, and an intact ventricular septum. We report a case of a 6-month-old female child with congenital heart disease diagnosed with Berry syndrome on cardiac computed tomography. Early diagnosis is critical as the condition is surgically correctable, with high mortality in untreated cases.