Congenital cervical dysgenesis is a rare mullerian anomaly occurring in 1 in 80,000 to 100,000 births and is thought to arise primarily from a defect in the elongation of the mullerian ducts. For decades, standard gynecologic practice for these patients has been the removal of the uterus to relieve the obstruction and conservative management is still a matter of debate. Presented here is a 17-year-old, nulligravid with congenital cervical dysgenesis who successfully underwent cervical canalization and cervico-vaginal anastomosis in a tertiary training institution. One month after surgery, the patient had normal menses and has been pain-free up to present. This paper concludes that a thorough investigation of patients with this anomaly is imperative and conservative management in carefully selected patients should be applied as first-line treatment option.

Human ; Female ; .