Philippine Journal of Reproductive Endocrinology and Infertility 2025;22(1):7-15

Chronic pelvic pain secondary to adenomyosis in Mayer-Rokitansky-Kuster-Hauser syndrome

Philip Judson M. de la Vega 1 ; Madonna Victoria S. Calderon-Domingo 1

Affiliations

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Country

Philippines

Language

English

Abstract

In Mayer-Rokitansky-K0ster-Hauser (MRKH) syndrome, the development of the uterus and some parts of the vagina is either completely absent or reduced. It is a rare congenital anomaly, and affects one in 4,000-5,000 female births and commonly presents as primary amenorrhea. Approximately 6% - 10% of these patients with MRKH syndrome report persistent pelvic pain, which may be attributed to the presence of myomas, endometriosis, adenomyosis or hematometra caused by a functioning endometrial tissue in a uterine remnant. This paper presents the case of a 37 year old nulligravid who experienced severe cyclic hypogastric pain, and was subsequently diagnosed with MRKH syndrome with adenomyosis. Clinical evaluation and definitive management of the index case are discussed.