Journal of the Korean Society of Echocardiography  2003;11(2):108-113

Two Cases of Spongy Myocardium Detected in Adult.

Woo Sin KIM 1 ; Jae Ha MANG ; Suk Joon PARK ; Ho Joon YOU ; Duc Ky LEE ; Mi Kyung KIM ; Seng Woon YANG ; Ju Sang KIM ; Jae Won SHIN ; Ho Joong YOUN

Affiliations

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Keywords

Sponge myocardium

Country

Republic of Korea

Language

Korean

Abstract

Isolated noncompaction of the left ventricular myocardium is a rare cardiac disorder due to an arrest in myocardial morphogenesis. It is characterized by prominent and excessive trabeculation in a ventricular wall segment, with deep intertrabecular spaces perfused from the ventricular cavity. Echocardiographic findings are important clues for the diagnosis. Clinical symptoms include signs of left ventricular systolic dysfunction even to the point of heart failure, ventricular arrhythmias, and embolic events. We describe two cases of isolated noncompaction of the myocardium, with ventricular tachycardia in one, and chest pain due to microvascular dysfunction in the other.