Korean Journal of Audiology  2013;17(3):142-147

doi:10.7874/kja.2013.17.3.142

Bilateral Ossiculoplasty in 1 Case of Achondroplasia.

Jongyoon JUNG 1 ; Chulwon YANG ; Sunkyu LEE ; June CHOI

Affiliations

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Keywords

Achondroplasia; Conductive hearing loss; Temporal bone; Ear ossicles; Ossicular prosthesis

Country

Republic of Korea

Language

English

Abstract

Achondroplasia is the most common skeletal dysplasia and it combines various complications with normal longevity. Hearing disturbance due to otitis media or an ossicular anomaly is one of the most common complications. Conductive hearing loss is suggested as the most common form of hearing loss. Temporal bone and middle ear structures are distorted in achondroplasia because of rotational change of the skull base. Authors experienced a case of an achondroplastic patient with bilateral hearing disturbance. We faced making a potential mistake during the previous operation but a favorable postoperative result occurred. Our experience could be helpful to other clinicians who face achondroplastic patients.