Nemaline Myopathy Presenting as Adult-onset Distal Myopathy.
Korean Journal of Clinical Neurophysiology.2016;18(1):31-33. doi:10.14253/kjcn.2016.18.1.31
Korean Journal of Clinical Neurophysiology
1999 to Present ISSN: 1229-6414
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Unilateral Optic Neuritis after Acute Hepatitis A.
Korean Journal of Clinical Neurophysiology.2016;18(1):28-30. doi:10.14253/kjcn.2016.18.1.28
Different Clinical Courses of Idiopathic Isolated Hypoglossal Nerve Palsy.
Korean Journal of Clinical Neurophysiology.2016;18(1):25-27. doi:10.14253/kjcn.2016.18.1.25
Primary Aldosteronism Presenting as Hypokalemia and Rhabdomyolysis.
Korean Journal of Clinical Neurophysiology.2016;18(1):21-24. doi:10.14253/kjcn.2016.18.1.21
Primary aldosteronism is one of the most common cause of secondary hypertension and can be accompanied with hypokalemia. Rhabdomyolysis with hypokalemia in primary aldosteronism has been rarely reported. We describe a patient of primary aldosteronism who presented with limb-girdle type weakness.
Humans ; Hyperaldosteronism* ; Hypertension ; Hypokalemia* ; Rhabdomyolysis*
Humans ; Hyperaldosteronism* ; Hypertension ; Hypokalemia* ; Rhabdomyolysis*
Myelin Water Fraction MRI in a Case of Clinically Probable Amyotrophic Lateral Sclerosis.
Korean Journal of Clinical Neurophysiology.2016;18(1):18-20. doi:10.14253/kjcn.2016.18.1.18
Amyotrophic lateral sclerosis (ALS) is a progressive motor neuron degenerative disease that clinically manifests both upper and lower motor neuron signs. However, it is unknown where and how the motor neuron degeneration begins, and conflicting hypotheses have been suggested. Recent advanced radiological techniques enable us to look into ALS neuropathology in vivo. Herein, we report a case with upper motor neuron-predominant ALS in whom the results of brain magnetic resonance imaging (MRI) and myelin water fraction MRI suggest axonal degeneration.
Amyotrophic Lateral Sclerosis* ; Axons ; Brain ; Magnetic Resonance Imaging* ; Motor Neurons ; Myelin Sheath* ; Neuropathology ; Pathology ; Water*
Amyotrophic Lateral Sclerosis* ; Axons ; Brain ; Magnetic Resonance Imaging* ; Motor Neurons ; Myelin Sheath* ; Neuropathology ; Pathology ; Water*
Pulmonary Thromboembolism after Intravenous Immunoglobulin Therapy in Guillain-Barre Syndrome.
Korean Journal of Clinical Neurophysiology.2016;18(1):14-17. doi:10.14253/kjcn.2016.18.1.14
Intravenous immunoglobulin (IVIG) is a safe treatment to treat various neurological disorders, but fatal thrombotic events as rare complications have been reported. A 54-year-old woman with Guillain-Barre syndrome complained of dyspnea during IVIG treatment. She was finally diagnosed with pulmonary thromboembolism. To the best of our knowledge, this is the first case of pulmonary thromboembolism associated with IVIG treatment in a Korean patient with Guillain-Barre syndrome.
Dyspnea ; Female ; Guillain-Barre Syndrome* ; Humans ; Immunization, Passive* ; Immunoglobulins* ; Immunoglobulins, Intravenous ; Middle Aged ; Nervous System Diseases ; Pulmonary Embolism*
Dyspnea ; Female ; Guillain-Barre Syndrome* ; Humans ; Immunization, Passive* ; Immunoglobulins* ; Immunoglobulins, Intravenous ; Middle Aged ; Nervous System Diseases ; Pulmonary Embolism*
Idiopathic Hypertrophic Cranial Pachymeningitis Masquerading as Tolosa-Hunt Syndrome.
Korean Journal of Clinical Neurophysiology.2016;18(1):11-13. doi:10.14253/kjcn.2016.18.1.11
Idiopathic hypertrophic cranial pachymeningitis (ICHP) is diffuse inflammatory process of the dura mater. ICHP can produce similar presentation with Tolosa-Hunt syndrome (THS) if it involves cavernous sinus. A-29-year old male with persistent headache and no definite neurologic dysfunction was noted. Two weeks later, he complained of ophthalmoplegia, and his symptoms were thought to be manifestations of THS. Brain magnetic resonance images revealed diffuse thickened, enhanced pachymeninges in left tentorium. The patient was diagnosed with IHCP. We report a IHCP patient who showed very similar presentation as THS.
Brain ; Cavernous Sinus ; Dura Mater ; Headache ; Humans ; Male ; Meningitis* ; Neurologic Manifestations ; Ophthalmoplegia ; Tolosa-Hunt Syndrome*
Brain ; Cavernous Sinus ; Dura Mater ; Headache ; Humans ; Male ; Meningitis* ; Neurologic Manifestations ; Ophthalmoplegia ; Tolosa-Hunt Syndrome*
Ultrasound Evaluation of Ulnar Neuropathy at the Elbow Caused by a Mass Lesion.
Korean Journal of Clinical Neurophysiology.2016;18(1):7-10. doi:10.14253/kjcn.2016.18.1.7
Ulnar neuropathy at the elbow (UNE) may seem easy to diagnose when the characteristic clinical manifestations are present, and electrodiagnostic studies have high sensitivity, although they are non-localizing in some cases and unable to reveal structural lesions. Ultrasonography is noninvasive and able to find the exact location of the lesion and visualize perineural structures. We present two cases of UNE in which we found hypoechoic mass lesions near medial epicondyle with ultrasonography and discuss its usefulness in diagnosis of UNE.
Diagnosis ; Elbow* ; Ulnar Neuropathies* ; Ultrasonography* ; United Nations
Diagnosis ; Elbow* ; Ulnar Neuropathies* ; Ultrasonography* ; United Nations
Korean Journal of Clinical Neurophysiology.2016;18(1):1-6. doi:10.14253/kjcn.2016.18.1.1
BACKGROUND: Moyamoya disease is characterized by a progressive stenosis or occlusion of the intracranial internal carotid artery and/or the proximal portion of the anterior cerebral artery and middle cerebral artery. Whether the onset time was childhood or adulthood, the bony carotid canal diameter might be different, but reflects the size of internal carotid artery passing through the bony carotid canal. In this study, we aimed to identify the relationship between bony carotid canal diameter and clinical manifestation. METHODS: 146 consecutive patients diagnosed with moyamoya disease by brain imaging studies were included. We measured the diameter of a transverse portion of bony carotid canal on bone window of a brain computed tomography(CT) image. Patients were divided into two groups, ischemic or hemorrhagic stroke according to clinical manifestation. As a result, 115 patients were included. The Suzuki stage was used as criteria for disease progression. RESULTS: Bony carotid canal diameter was 3.6 ± 0.5 (right) and 3.6 ± 0.4 (left) in the hemorrhagic stroke group, and 3.7 ± 0.4 (right) and 3.6 ± 0.4 (left) in the ischemic stroke group. The bony carotid canal diameter of the moyamoya vessels (3.6 mm) was smaller than the diameter of non-moyamoya vessels (3.8 mm), significantly (p= 0.042). However, there was no difference in the collateral patterns and clinical manifestation in a comparison of both groups. CONCLUSIONS: In our study, there was no significant difference of clinical manifestations and collateral patterns depend on the bony carotid canal diameter in patients with moyamoya disease. These findings suggest that the clinical presentations of moyamoya disease are not related to the onset time of the disease.
Anterior Cerebral Artery ; Brain ; Carotid Artery, Internal ; Constriction, Pathologic ; Disease Progression ; Humans ; Middle Cerebral Artery ; Moyamoya Disease* ; Neuroimaging ; Stroke
Anterior Cerebral Artery ; Brain ; Carotid Artery, Internal ; Constriction, Pathologic ; Disease Progression ; Humans ; Middle Cerebral Artery ; Moyamoya Disease* ; Neuroimaging ; Stroke
Korean Journal of Clinical Neurophysiology.2014;16(1):21-26. doi:10.14253/kjcn.2014.16.1.21
BACKGROUND: Electrophysiological study has been known as a useful method to evaluate the therapeutic effect of operation in idiopathic carpal tunnel syndrome (CTS). The purpose of this study was to evaluate the clinical and electrophysiological changes after carpal tunnel release (CTR) compared to the preoperative results. METHODS: We analyzed the changes of nerve conduction study (NCS) before and after minimal open carpal tunnel release in 18 patients (25 hands) with CTS. Follow-up study was performed over 6 months after operation. RESULTS: Clinical improvement was seen in all cases after CTR. In contrast, electrophysiological improvement was various depending on the parameters; the mean median sensory latency and nerve conduction velocity (NCV) improved significantly (p = 0.001). The mean median motor latency also improved, but NCV and compound muscle action potential (CMAP) amplitude did not change. The extent of improvement was evident in moderate CTS, but not in severe CTS. CONCLUSIONS: In this preliminary study, all subjects who underwent CTR achieved a clinical relief along with a significant improvement of electrophysiological parameters such as median sensory latency, sensory NCV and median distal motor latency. After CTR, a number of cases with mild to moderate CTS showed a prominent improvement of clinical and electrophysiological parameters, while fewer improvements were seen in severe CTS, although it did not reach the statistical significance.
Action Potentials ; Carpal Tunnel Syndrome ; Electrophysiology ; Follow-Up Studies ; Hand* ; Humans ; Median Nerve ; Neural Conduction
Action Potentials ; Carpal Tunnel Syndrome ; Electrophysiology ; Follow-Up Studies ; Hand* ; Humans ; Median Nerve ; Neural Conduction
Country
Republic of Korea
Publisher
Korean Society of Clinical Neurophysiology
ElectronicLinks
http://synapse.koreamed.org/LinkX.php?code=1208KJCNEditor-in-chief
Jong-Seok Bae
Abbreviation
Korean Journal of Clinical Neurophysiology
Vernacular Journal Title
대한임상신경생리학회지
ISSN
1229-6414
EISSN
2288-1026
Year Approved
2013
Current Indexing Status
Currently Indexed
Start Year
1999
Description
Korean Journal of Clinical Neurophysiology (Korean J Clin Neurophysiol) is the official Journal of The Korean Society of Clinical Neurophysiology, published twice a year in Korean or English. The journal publishes full-length original paper, case report, invited reviews, controversies in clinical neurophysiology, images in clinical neurophysiology, and other articles requested by editorial board. The journal aims to publish evidence-based, scientific and creative research materials in the field of clinical neurophysiology, clinical neurology, and neuroscience. All submitted manuscripts should be original and should not be considered by other scientific journals for publication at the same time.
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