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Jeong Keon LIM ; Dang Do YI ; Chung kyu SUH ; Young Choon PARK ; Yeung Ju BYUN

Journal of the Korean Neurological Association.1989;7(1):172-177.

Huntington's disease(HD) is a neurcdegenerative disorder caused by a highly penetrant autosomal dominant genetic defect. It is characterized by adult onset progressive chorea, psychological change, and dementia with relentless deterioration. Until now the reported cases are very rare in Korea, so we presented here two cases of definite HD.
Adult ; Chorea ; Dementia ; Humans ; Huntington Disease* ; Korea

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Two Cases of Reversible Leukoencephalopathy, Caused by 5-Fluorouracil, Presenting as Akinetic Mutism.

Se Jin LEE ; Kyung Chan CHOI ; Jung Sang HAH ; Yeung Ju BYUN ; Choong Seo PARK

Journal of the Korean Neurological Association.1989;7(1):165-171.

We experinced 2 cases of reversible leukoencephalopathy, caused by 5-Fluorouracil derivatives(carmoful), presenting as akinetic mutism. Each patient was diagnosed as colon cancer and stomach cancer respectively and received operations. Their outcome was good without metastatic evidences, and carmoful was started orally 400mg in 1 case and 600mg in the other. Their clinical pictures were akinetic mutism, one and two months after the administration of carmoful. There were no metastatic lesions in the brain CT but bilaterally symmetric diffuse low densities of cerebral whites matter, predominantly in the frontal area, were noted. Carmoful was discontinued and replaced by conservative treatment. One and two months later, their clinical symptoms improved without specific treatment. Follow up brain CT was done in case 2, which revealed attenuation of the previous low densities.
Akinetic Mutism* ; Brain ; Colonic Neoplasms ; Fluorouracil* ; Follow-Up Studies ; Humans ; Leukoencephalopathies* ; Stomach Neoplasms

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Two Cases of Unverricht-Lundborg Disease.

Sang Kun LEE ; Seol Heui HAN ; Jae Kyu RHO ; Sang Bok LEE ; Ho Jin MYUNG

Journal of the Korean Neurological Association.1989;7(1):157-164.

Unverricht-Lundborg disease(Baltic myoclonus) is one of the major causes of progressive myoclonus epilepsy. It is characterized by stimulus sensitive myoclonic seizure, generaized tonic-clonic seizure, generally synchronous polyspike and wave discharges on EEG and absence of severe or early dementia. It has usually been described in the countries around the Baltic area. But recently, it is regarded as the most common form of progressive myoclonus epilepsy in the other countries as well. We report, with the review of the literature, two patients who showed the typical features of this disorder.
Dementia ; Electroencephalography ; Humans ; Myoclonic Epilepsies, Progressive ; Seizures ; Unverricht-Lundborg Syndrome*

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Mirror-writing" in the Patient of Intracerebral Hemorrhage.

Hee Tae KIM ; Hong Ki SONG ; Ju Han KIM ; Kyung Cheon CHUNG ; Myung Ho KIM

Journal of the Korean Neurological Association.1989;7(1):150-156.

"Mirror-writing" is stript that runs in the direction opposite to normal with the individual letters also reversal. Several theories, including motor, visual dominance, spatial disorientation and supplementary motor hypotheses, have been proposed to explain "mirror-writng". With reviewing some of literatures, we present two cases of "mirror-writing" in association with bilateral basal ganglia hemorrhage and right frontal hematoma, respectively.
Basal Ganglia Hemorrhage ; Cerebral Hemorrhage* ; Hematoma ; Humans

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A Case Report of Facial Diplegia Associated with Acute Viral Hepatitis type B.

Mee Yeong PARK ; Se Jin LEE ; Jeng Sang HAH ; Yeung Ju BYUN ; Choong Seo PARK

Journal of the Korean Neurological Association.1989;7(1):145-149.

The Neuropsychiatric complications in acute viral hepatitis are uncommon. Despite the wide spread occurrence of this disease. Various complications of central and peripheral nervous involvement may arise during the course of viral hepatitis. Encephalitis, meningitis, neuritis, myelitis and mental disturbances such as depression, euphoria and insomnia complicating viral hepatitis has been reported several literatures. Also, bilateral facial nerve palsy is seen very infrequently in clinical practice and has an annual incidence of approximately 0.01% per total facial nerve palsy. The isolated cranial nerve palsy, especially facial nerve. Complicated by viral hepatitis has been suggested very rarely. This combination of bilateral facial nerve palsy and viral hepatitis B seems to be two phases of same disease. However, there were no such reports in Korea until now. Therefore, We present a case of bilateral peipheral facial nerve palsy associated with acute viral hepatitis type B.
Cranial Nerve Diseases ; Depression ; Encephalitis ; Euphoria ; Facial Nerve ; Hepatitis B ; Hepatitis* ; Incidence ; Korea ; Meningitis ; Myelitis ; Neuritis ; Paralysis ; Sleep Initiation and Maintenance Disorders

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A Case of Dern atomyositis Associated with Primary Hepatoma.

Byeong Hoon LIM ; Choong Kun HA

Journal of the Korean Neurological Association.1989;7(1):140-144.

Dematomyositis is an inflammatory cutaneo-muscular disease of unknown etiology, characterized by symmetrical proximal muscle weakness and typical dermatologic manifestation. Association with systemic maligmancy has been reported in many literatures, but the relationship of dermatomyositis to internal malignancy remains controversial. In Korea, several cases of dermatomyositis or polymyositis associated with malignant neoplasm were reported. Dermatomyositis or polymyositis associated with primary hepatoma has not been reported, Recently authors experienced a patient with dermatomyositis associated with primary hepatoma, and present the case with review of literatures. This may be the first report in Korea.
Carcinoma, Hepatocellular* ; Dermatomyositis ; Humans ; Korea ; Muscle Weakness ; Polymyositis

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A Case of Down Syndrome with Atlanto-axial Dislocation.

Won Yong LEE ; Kwang Kuk KIM ; Jong Sung KIM ; Kwang Woo LEE ; Jae Kyu RHO ; Sang Bok LEE ; Hojin MYUNG

Journal of the Korean Neurological Association.1989;7(1):131-139.

Atlanto-axial instability in children with Down syndrome(trisomy 21) has become a wel! Known entity and it has been reported frequently since it was first reported over 25 years ago. However, symtomatic atlanto-axial dislocation associated with cord compression is relatively rare and it had seldom been reported. We recently experienced a 14-year-old mongoloid female with progressive quadriparesis, who have no prior cervical inflammation and we detected atlanto-axial dislocation with ossculum terminale and cord compression through radiological evaluations. We report a case of symptomatic atlanto-axial dislocation in Down syndrome with review.
Adolescent ; Child ; Dislocations* ; Down Syndrome* ; Female ; Humans ; Inflammation ; Quadriplegia

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A Case of Musicogenic Epilepsy.

Yeung Ju BYUN ; Jeung Sang HAH ; Choong Seo PARK

Journal of the Korean Neurological Association.1989;7(1):123-130.

In Patients subject to convulsions the attacks occur sporadically, and the factors reponsible for precipitation of a seizure at any given time are usually unknown. In a small number of patients certain sensory stimuli may consistently initiate an attack. The sensory modality involved varies in different patients: however, the entire group has been referred to by the term 'reflex epilepsy.' In certain rare instances, listening to music produces seizures and this subdivision of reflex epilepsy has been called "musicogenic epilepsy". By the Critchley, in 1937, several particular types of musical stimuli were reported, but frequency of such stmuli was much rare and there has been no report yet in Korea. This 40 years old fernale patient revealed a ternporal lobe seizure, which appeared whenever listened to old korean popular songs. The etiology was not known and the response to anti-epileptic drugs was good.
Adult ; Epilepsy, Reflex* ; Humans ; Korea ; Music ; Seizures

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The Value of the Radio-isotope Angiography in Reflex Sympathetic Dystrophy.

Young Jin LEE ; Myung Sik LEE ; Il Saing CHOI ; Tae Sub CHUNG ; Young Seok LEE

Journal of the Korean Neurological Association.1989;7(1):114-122.

No abstract available.
Angiography* ; Reflex Sympathetic Dystrophy* ; Reflex*

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A case of Neurosarcoidosis with Facial Diplegia and of the Suspected Cardiac Involvement.

Keun Seop BAEK ; Kwang Ho LEE ; Yeon Tae JEUNG

Journal of the Korean Neurological Association.1989;7(1):108-113.

Sarcoidosis is multisystem granulomatous disorder of unknown etiology presenting most freguently with bilateral hilar lymphadenopathy, pulmonary infiitration, and skin or eye lesion. Nervous system is involoved clinically in approximately 5% of cases. Cranial neuropathy is the most frequent problem, and a peripheral facial nerve palsy is the single most common abnormlality which is often bilateral. About 12 cases of sarcoidosis have been reported in Korea but there was no case of neurosarcoidosis. We report a case of neurosarcoidosis manifested by facial diplegia and with bilateral hilar enlargement verified by transbronchial lung biopsy. And her heart is suspected to be involved with sarcoidosis, too.
Biopsy ; Cranial Nerve Diseases ; Facial Nerve ; Heart ; Korea ; Lung ; Lymphatic Diseases ; Nervous System ; Paralysis ; Sarcoidosis ; Skin

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