Philippine Journal of Reproductive Endocrinology and Infertility 2019;16(1):22-28

Uterine didelphys with unilateral cervicovaginal agenesis: A case report.

Apple Mae G. SIMPAN 1 ; Marian C. DICHOSO 1

Affiliations

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Keywords

Cervicovaginal Agenesis; Mullerian Anomalies; Uterine Didelphys; Didelphic Uterus

Country

Philippines

Language

English

Abstract

Unilateral cervicovaginal agenesis in a didelphic uterus is an extremely rare congenital anomaly. Women born with this anomaly present with menarche associated with progressive dysmenorrhea and symptoms of worsening endometriosis. Presented here is a case of a 12 year old nulligravid who presented with progressive cyclic abdominal pain. Physical examination revealed a tender large right adnexal mass and presence of a vaginal canal and cervix tilted to the left. Sonography showed the presence of uterine didelphys, right hematosalpinx and hematocolpos. Preoperative impression was outflow tract obstruction probably due to Herlyn Werner-Wunderlich syndrome. However, intraoperatively, it was discovered this was a case of uterine didelphys with outflow tract obstruction of the right hemiuterus due to unilateral cervicovaginal agenesis and ipsilateral renal agenesis.