Archives of Craniofacial Surgery  2014;15(3):125-128

doi:10.7181/acfs.2014.15.3.125

Malignant Peripheral Nerve Sheath Tumor in Frontal Sinus, Orbital Cavity and Ethmoid Cavity.

Jeong Hwan LEE 1 ; Nam Gyun KIM ; Kyung Suk LEE ; Jun Sik KIM

Affiliations

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Keywords

Malignant peripheral nerve sheath tumors; Head and neck neoplasms; Frontal sinus; Orbital area

Country

Republic of Korea

Language

English

Abstract

Malignant peripheral nerve sheath tumors are extremely rare soft tissue sarcomas. Among various locations, the trunk and extremities are the most commonly involved sites, with only 15% of such lesions occuring in head and neck region. Here, we report a case of a 74-year-old male who presented with forehead swelling and right eye deviation. Computed tomography images revealed a tumor involving the frontal sinus, ethmoid sinus, and the orbital cavity. The patient underwent a surgical excision of the lesion, which histopathological examination revealed to be a malignant peripheral nerve sheath tumor.