Korean Journal of Gynecologic Oncology  2007;18(2):155-159

A case of recurrent aggressive angiomyxoma of the vulva in the adolescence.

Joo Yuen RYU 1 ; Mi Sun PARK ; Chang Jae LEE ; Kyung Rak SON

Affiliations

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Keywords

Aggressive angiomyxoma; GnRH agonist; Radiation therapy

Country

Republic of Korea

Language

Korean

Abstract

Aggressive angiomyxoma is a rare, locally infiltrative soft tissue tumor that usually arises in the vulvoperitoneal region of young female. Frequent relapses are common. Clinicians should consider the diagnosis of aggressive angiomyxoma when a patient presents with an atypical vulvoperineal mass, because an incorrect diagnosis may lead to repeated surgical procedures. Treatment is wide surgical excision. Medical management with a GnRH agonist and radiation therapy with total dose of 60 Gy may be helpful adjuvant treatment in recurrent aggressive angiomyxoma. We experienced a case of recurrent aggressive angiomyxoma and report it with a brief review of literatures.