Obstetrics & Gynecology Science  2014;57(1):73-76

doi:10.5468/ogs.2014.57.1.73

An unusual prenatal manifestation of a huge congenital cystic adenomatoid malformation with favorable perinatal outcome.

Hye Jin SUK 1 ; Hye Sung WON ; Eun Jung LEE ; Mi Young LEE

Affiliations

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Keywords

Congenital; Cystic adenomatoid malformation of lung; Fetal therapies; Hydrops fetalis; Prenatal diagnosis

Country

Republic of Korea

Language

English

Abstract

Congenital cystic adenomatoid malformation (CCAM) is a rare condition which is easily detectable by prenatal ultrasonography. Fetuses with large CCAMs associating with hydrops are predisposed to perinatal mortality, therefore prenatal intervention is required. While macrocystic CCAM is treated prenatally by thoracentesis or thoraco-amniotic shunt, microcystic or mixed CCAM is difficult to manage in the fetus. In these latter lesions, fetal lobectomy, sclerotherapy, or laser ablation was used to treat lesions directly. We present an unusual prenatal case of mixed CCAM associating with hydrops and marked ascites, which was conservatively managed with prenatal abdomino-amniotic shunting and successfully treated by postnatal surgery.