Journal of the Korean Radiological Society  2003;49(6):503-506

doi:10.3348/jkrs.2003.49.6.503

Radiologic Findings of Cystic Fibrosis in a Korean Child at Follow Up Study: Case Report.

Il Soo JANG 1 ; Choong Ki PARK ; Seok Chol JEON ; Yo Won CHOI ; Dong Woo PARK ; Yongsoo KIM ; Young Sun KIM ; You Hern AHN

Affiliations

+expand

Keywords

Fibrosis, cystic; Lung; Respiratory distress syndrome, in infants and children

Country

Republic of Korea

Language

Korean

Abstract

Cystic fibrosis is a hereditary disease involving recessive transmission. The fundamental abnormality consists of the production of abnormal secretion from a variety of exocrine glands such as salivary and sweat glands and those of the pancreas, colon, and tracheobronchial trees. Cystic fibrosis is the most common lethal genetically transmitted disease among whites, but is uncommon in Asians, including Koreans. Although a case involving a Korean was reported in 1988, the focus was diagnosis rather than the radiological findings. In the case of cystic fibrosis we now describe, the focus is inverted: we enphasise the reported in 1988, focusing on radiologic findings.