Clinical Pediatric Hematology-Oncology  2011;18(1):66-69

A Case of Pediatric Solid Pseudopapillary Tumor of the Pancreas Treated with Gemcitabine

Ye Jee SHIM 1 ; Ji Hyun KANG ; Kun Soo LEE

Affiliations

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Keywords

Pancreas; Metastasis; Gemcitabine

Country

Republic of Korea

Language

English

Abstract

Solid pseudopapillary tumors of the pancreas (SPTPs) are rare tumors with limited malignant potential; they are mainly diagnosed in young women. Complete surgical resection of the tumor is usually possible and patients have an excellent prognosis. However, local invasion and distant metastases have been reported in about 10-20% of patients with SPTPs; these patients require supplementary management for long-term survival. Here, we report a pediatric patient with inoperable SPTP unresponsive to neoadjuvant chemotherapy using cisplatin, ifosfamide, and etoposide which had spread to other organs. Subtotal resection of the primary tumor, radiofrequency ablation, radiotherapy, and adjuvant chemotherapy using gemcitabine were done to control this progressive SPTP.