Journal of Liver Cancer  2016;16(2):151-154

doi:10.17998/jlc.2016.16.2.151

Hepatic Immunoglobulin G4-related Inflammatory Pseudotumor Mimicking Hepatocellular Carcinoma.

Seung Heon KANG 1 ; Sang Hoon PARK ; Ho Hyun PARK ; Jeong Rok LEE ; Won Hyeok CHOE ; So Dug LIM ; Soon Young KO

Affiliations

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Keywords

Hepatocellular carcinoma; Inflammatory pseudotumor

Country

Republic of Korea

Language

Korean

Abstract

Immunoglobulin G4-related disease is a recently recognized entity characterized by a mass-forming or regional lesion that contains an extensive infiltration of IgG4-producing plasma cells with dense fibrosis. Immunoglobulin G4-related disease can affect any organ system, but solitary hepatic lesion of Immunoglobulin G4-related disease is very rare. This entity mimics primary malignant hepatic tumor, such as hepatocellular carcinoma or intrahepatic cholangiocarcinoma. We experienced a case of hepatic IgG4-related inflammatory pseudotumor in a 50-year-old woman, mimicking hepatocellular carcinoma.