Korean Journal of Pediatric Hematology-Oncology  2004;11(2):260-264

A Case of Alveolar Soft Part Sarcoma in a Child.

Jee Yong KIM 1 ; Geun Young LEE ; Ok Ran SHIN ; Ju Mee KANG ; Pil Sang JANG ; Dong Un KIM ; Young Hoon KIM ; Jin Tack KIM

Affiliations

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Keywords

Alveolar soft part sarcoma; Children

Country

Republic of Korea

Language

Korean

Abstract

Alveolar soft part sarcoma (ASPS) is a rare soft tissue tumor that accounts for 5% of pediatric non-rhabdomyosarcoma soft tissue sarcomas. The disease presents as a indolent asymptomatic mass and affects primarily younger patients. The clinical course is often indolent and late metastases can develop even after prolonged disease-free intervals. Radiotherapy and chemotherapy play a very limited role in the treatment. We report a pediatric case of ASPS with a brief review of the literature.