Journal of the Korean Society of Pediatric Nephrology  2002;6(1):92-96

A Case of Oligomeganephronia of the Solitary Kidney, Presented with Isolated Proteinuria.

Soeun PARK 1 ; Jung Won LEE ; Su Jin CHO ; Eun Sun YOO ; Hae Soon KIM ; Soon Hee SUNG ; Seung Joo LEE

Affiliations

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Keywords

Oligomeganephronia; Solitary kidney; Proteinuria

Country

Republic of Korea

Language

Korean

Abstract

Oligomeganephronia is rare congenital anomaly characterized by striking reduction of the number of nephrons, which are markedly hypertrophied in renal hypoplasia. Since the first description of oligomeganephronia in bilateral renal hypoplasia in 1962, dozens of cases were reported. Van Acker reported the first case of oligomeganephronia developed in the solitary kidney and 8 cases were searched in the literature. We report a case of oligomeganephronia in the solitary kidney in 13 years old boy, presented with isolated proteinuria as a first case in Korea.