Journal of the Korean Society of Pediatric Nephrology  2013;17(1):25-28

A Female Infant with Segmental Multicystic Dysplastic Kidney.

Jun Ho LEE 1 ; Moon Kyu KIM

Affiliations

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Keywords

Computed tomography; Multicystic renal mass; Renal ultrasonography; Segmental multicystic dysplastic kidney

Country

Republic of Korea

Language

English

Abstract

There have only been 35 pediatric cases and one adult case reported on segmental multicystic dysplastic kidney (MCDK) from our search in PubMed, including 19 cases detected antenatally. There is little documentation of segmental MCDK, particularly concerning its natural history. Segmental MCDK can be presented atypically, making diagnosis more difficult. We report an another case with segmental MCDK. Multicystic abdominal mass detected on antenatal sonogram in this infant was diagnosed as segmental MCDK by renal ultrasonography and computed tomography. If a definitive diagnosis of segmental MCDK can be made on imaging, surgery is not required for a diagnostic biopsy.