Korean Journal of Pancreas and Biliary Tract  2014;19(1):26-30

doi:10.15279/kpba.2014.19.1.26

IgG4-related Sclerosing Cholangitis Presented as a Mass in the Liver.

Ji Yeoun KIM 1 ; Kyo Sang YOO ; Young Ha OH ; Jong Min CHOI ; Sang Ki LEE ; Yoomi YEO ; Soon Woo HWANG ; Hye Jin YOON

Affiliations

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Keywords

IgG4-related sclerosing cholangitis; Inflammatory pseudotumor

Country

Republic of Korea

Language

Korean

Abstract

Autoimmune pancreatitis or IgG4-related sclerosing cholangitis often involves the liver. Most common lesion involving the liver is shown as mass or masses often referred as inflammatory pseudotumor. Inflammatory pseudotumor usually needs to be discriminated with malignancy. Here we report a case of IgG4-related sclerosing cholangitis with liver involvement presented as a mass. It was proven by biopsy and did not show any evidence of autoimmune pancreatitis. The mass infiltrated around the portal tract and portal vein thrombosis was also present.