Journal of Korean Epilepsy Society  2004;8(2):163-166

A Case of Idiopathic Localized Hypertrophic Pachymeningitis Presented with Partial Seizures.

Yoon Jeong CHOI 1 ; Sook Hui KIM ; Jee Young KIM ; Yong Jae CHO ; Shi Nae LEE ; Heasoo KOO ; Hyang Woon LEE

Affiliations

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Keywords

Idiopathic hypertrophic pachymeningitis; Partial seizures; Lesionectomy

Country

Republic of Korea

Language

Korean

Abstract

Idiopathic hypertrophic pachymeningitis is a clinical disorder caused by a localized or diffuse thickening of the dura mater, with an associated chronic inflammation. This can be diagnosed when there is no evidence of other etiologies such as trauma, infection, tumors, and Wegener's disease. Clinical manifestations are chronic headache with or without neurological manifestations such as cranial nerve palsies, cerebellar ataxia, neuro-ophthalmologic complications, and rarely clinical seizures. We described a patient with simple partial seizures with focal sensory and motor symptoms in the right hand as an initial and the only clinical manifestation, accompanied by a tumor-like lesion in the left parietal convexity on brain MRI. The patient underwent a lesionectomy, and the seizures have been well controlled so far without immunosuppressant treatment.