Korean Journal of Pediatrics  2008;51(9):1018-1022

doi:10.3345/kjp.2008.51.9.1018

A case of testicular adrenal rest tumor in a male child with congenital adrenal hyperplasia.

Joo Hwa KIM 1 ; Kyong Ah YUN ; Choong Ho SHIN ; Sei Won YANG

Affiliations

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Keywords

Testicular neoplasms; Adrenal rest tumor; Child; Congenital adrenal hyperplasia; Steroid; 21-hydroxylase

Country

Republic of Korea

Language

English

Abstract

Testicular adrenal rest tumors are a well-known complication in male patients with congenital adrenal hyperplasia. Corticosteroid suppressive therapy usually results in the regression of these tumors. We describe a patient with 21-hydroxylase deficiency who developed bilateral testicular masses. Despite steroid suppressive therapy, the tumors did not regress and hormonal control was poor. Consequently, bilateral partial orchiectomies were performed.