Tuberculosis and Respiratory Diseases  2001;50(1):127-131

doi:10.4046/trd.2001.50.1.127

Pulmonary Lymphangioleiomyomatosis with Chylous Pleural Effusion.

Byung Joon PARK ; Jae Hwa CHO ; Tae Hoon MOON ; Sang Joon PARK ; Jung Seon RYU ; Hong Lyeol LEE ; Seung Min KWAK ; Chul Ho CHO

Keywords

Lymphangioleiomyomatosis; Chylous pleural effusion

Country

Republic of Korea

Language

Korean

Abstract

Pulmonary lymphangioleiomyomatosis is a disease involving the proliferation of atypical smooth muscle cells trom the perilymphatics, peribronchial and perivascular region of the lung and the retroperitneum. The disease usually affects women of child-bearing age. We recently experienced a case of pulmonary lymphangioleiomyomatosis in a 31-year-old women who had suffered from a chylous pleural effusion. Histologic confirmation of lymphangioleiomyomatosis was made upon a video-associated thoracoscopic lung biopsy. Here we report this case with a brief review of the literature.