Korean Journal of Pediatric Hematology-Oncology  2005;12(1):120-124

A Case of Congenital Hepatoblastoma.

Min Jung SUNG 1 ; Jae Hong PARK ; Hae Young KIM ; Young Tak LIM

Affiliations

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Keywords

Congenital hepatoblastoma; Worse prognosis

Country

Republic of Korea

Language

Korean

Abstract

Hepatoblastoma is the most common primary malignant hepatic tumor in infancy and childhood. But congenital hepatoblastomas are extremely rare and show distinctive, but important features when compared with tumors diagnosed in children beyond the neonatal age. They have different clinical presentations, higher incidence of pure fetal histology, significant risk for systemic metastasis, and worse outcome. The treatment of congenital hepatoblastoma should be the same as in older children, i.e., primary chemotherapy with delayed resection. We report a case of congenital hepatoblastoma in a 29-day-old boy who was known to have a well-defined ovoid hypoechoic mass at liver demonstrated by fetal sonography.