Korean Journal of Pediatric Hematology-Oncology  2005;12(1):125-130

A Case of Incidentaloma Compromising of Pheochromocytoma and Adrenocortical Adenoma in an Infant.

Ji Hea KANG 1 ; Woe Sook YOON ; Jae Sun PARK ; Jong Cheol KIM ; Young Ok KIM ; Won Duk KIM

Affiliations

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Keywords

Incidentaloma; Pheochromocytoma; Adrenocortical adenoma

Country

Republic of Korea

Language

Korean

Abstract

Pheochromacytoma, although occasionally present with adrenal cortical hyperfunction, is rarely associated with nonfunctioning adrenal cortical tumor. To our knowledge, eight cases of phemchromocytoma associated with adrenocortical adenoma have been reported in the literature, including a case in a Korean adult female. An adrenal mass is considered an incidentaloma when there is no history or physical findings suggesting an adrenal functional disorder or tumor. The majority of adrenal masses are nonfunctioning adrenocortical adenomas. In our case, left adrenal mass was found incidentally by ultrasonography after birth, done because of mother's oligohydroamnios. Abdomial CT study revealed an adrenal tumor, and a surgical resection was performed. The specimen showed a coincident pheochromocytoma and adrenocortical adenoma. The patient seems to be the first case of coexistence of nonfunctioning pheochromocytoma and adrenocortical adenoma in one adrenal tumor. We report this case with the review of literatures.