Korean Journal of Clinical Neurophysiology  2015;17(2):76-79

doi:10.14253/kjcn.2015.17.2.76

Recurrent Myelopathy in a Patient with Klippel-Trenaunay Syndrome.

Yue Kyung KIM 1 ; Young In EOM ; In Soo JOO

Affiliations

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Keywords

Myelopathy; Klippel-Trenaunay syndrome; Vascular malformation

Country

Republic of Korea

Language

Korean

Abstract

Klippel-Trenaunay syndrome (KTS) is a rare congenital malformation syndrome involving blood and lymph vessels, which is characterized by triad of cutaneous hemangioma, venous varicosities, and overgrowth of the affected limbs. Because vascular malformation in KTS can be located anywhere except the face and brain, the clinical presentation could be extremely variable. But there are only rare case reports that KTS is associated with spinal cord lesion. We report a case of recurrent myelopathy in a patient with KTS.