Journal of Dental Anesthesia and Pain Medicine  2017;17(3):215-217

doi:10.17245/jdapm.2017.17.3.215

Anesthetic management of a patient with branchio-oto-renal syndrome.

Masanori TSUKAMOTO 1 ; Takeshi YOKOYAMA

Affiliations

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Keywords

Branchio-oto-renal Syndrome; Congenital Heart Disease; Difficult Airway; General Anesthesia; Renal Failure

Country

Republic of Korea

Language

English

Abstract

Branchio-oto-renal syndrome (BOR) is a rare autosomal dominant disorder. The features include branchial cysts, hearing loss, ear malformation, preauricular pits, retrognathia, congenital heart disease, and renal abnormalities. However, anesthetic management of these patients has seldom been reported. We report a case in which general anesthesia was performed for dental treatment in a patient with BOR. Airway management, renal function, and hemodynamic changes can be of critical concern during anesthetic management. A 13-year-old girl diagnosed with BOR had severe right hearing loss, right external ear malformation, renal abnormalities, and postoperative patent ductus arteriosus (PDA). Dental extraction under general anesthesia was scheduled for a supernumerary tooth. The procedure was completed with sufficient urine volume, adequate airway management, and stable hemodynamics.