Journal of Menopausal Medicine  2013;19(3):135-138

doi:10.6118/jmm.2013.19.3.135

Uterine Adenomyosis Which Developed from Hypoplastic Uterus in Postmenopausal Woman with Mayer-Rokitansky-Kuster-Hauser Syndrome: A Case Report.

Sungwook CHUN 1 ; Yeon Mee KIM ; Yong Il JI

Affiliations

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Keywords

Adenomyosis; Mayer-Rokitansky-Kuster-Hauser syndrome; Uterine adenomyosis

Country

Republic of Korea

Language

English

Abstract

Mayer-Rokitansky-Kuster-Hauser syndrome (MRKHS) is characterized by vaginal agenesis with variable Mullerian duct abnormalities. We report here a case of uterine adenomyosis which developed from a hypoplastic uterus in a patient with MRKHS. A 55-year-old postmenopausal woman visited a university hospital for pelvic mass. She had underwent vaginoplasty via the McIndoe procedure for MRKHS at 15 years of age. Pelvic magnetic resonance imaging showed a 5.4 x 4.8 x 4.7 cm mass suspicious for a uterine myoma. She received total abdominal hysterectomy with bilateral salpingo-oophorectomy, and neither the cervix nor endometrium was found grossly in the surgical specimen. The final histologic diagnosis was uterine adenomyosis.