Soonchunhyang Medical Science  2017;23(1):81-84

Rosai-Dorfman Disease of 4-Year-Old Girl.

Jun Seak GANG 1 ; Young Chang KIM ; Young Man LEE ; Junhun CHO ; Won Suk SUH ; Kyeong Bae PARK

Affiliations

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Keywords

Lymphadenopathy; Child; Histiocytosis

Country

Republic of Korea

Language

Korean

Abstract

Rosai-Dorfman disease also known as sinus histiocytosis with massive lymphadenopathy is a benign, rare systemic disease characterized by a histiocyte proliferation which presents with lymphadenopathy. We report a case of a 4-year-old girl who presented with recurrent cervical lymphadenopathy with tenderness, without any other symptoms. After 1 month of medical treatment, her lymphadenopathy still remained, so we performed complete excision and biopsy. She was diagnosed on cytology as a case of Rosai-Dorfman disease. She responded well to become asymptomatic without recurrence by 1 month.