Korean Journal of Pediatric Gastroenterology and Nutrition  2001;4(1):113-119

A Case of Mesenchymal Hamartoma Associated with Biliary Atresia.

Kyung Dan CHOI 1 ; Jeong Kee SEO ; Eon Woo SHIN ; Jae Sung KO ; Woo Sun KIM ; Young Su PARK ; Kyung Hoon KANG ; Je Geun CHI

Affiliations

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Keywords

Mesenchymal hamartoma; Liver; Biliary atresia; Infant

Country

Republic of Korea

Language

Korean

Abstract

Mesenchymal hamartoma is an uncommon benign tumor usually found in childhood, especially during the first two years of life. The tumor consists of a solid component and multiple cyst. Without treatment, these lesions can grow to an enormous size. We experienced a case of mesenchymal hamartoma which was found incidentally, in a 8 month old girl who had ascending cholangitis after Kasai operation due to biliary atresia. On abdominal ultrasonography and CT, there was a well-defined homogeneous small echogenic mass in the right lobe of the liver with cirrhosis. Five months later, she underwent liver transplantation. Gross picture of the resected liver showed a dark greenish pigmented solid mass in the right lobe of the cirrhotic liver. Microscopic findings showed reactive mesenchyma and epithelial overgrowth.