Yeungnam University Journal of Medicine  1998;15(2):381-390

doi:10.12701/yujm.1998.15.2.381

A case of incontinentia pigmenti developed in a male newborn infant.

Min Jeong CHO 1 ; Son Moon SHIN ; Han Ku MOON

Affiliations

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Keywords

incontinentia pigmenti; male

Country

Republic of Korea

Language

Korean

Abstract

Incontinentia pigmenti is characterized by irregular linear blisters with erythematous lesions which are developed from birth or later, verrucous papules on the extremities which are noted after a few weeks or months, and the appearnace of streaks, spots and swirls of hyperpigmentation. This disorder is known as a systemic disorder caused by a defect at the developmental stage of organs originated from ectoderm or mesoderm. We experienced an incontinentia pigmenti in a male newborn infant who did not have any family history and had cutaneous lesions, which were in bullous and verucous stages, ophthalmic problems, and neurologic abnormalities.