Journal of Rheumatic Diseases  2013;20(4):247-250

doi:10.4078/jrd.2013.20.4.247

A Case of Acroosteolysis in Primary Hypertrophic Osteoarthropathy.

Hyun Jeong LEE 1 ; Hong Jae KIM ; Chul Gu HWANG ; Jae Hoon CHOI ; Eun Jin KANG

Affiliations

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Keywords

Primary hypertrophic osteoarthropathy; Acroosteolysis

Country

Republic of Korea

Language

Korean

Abstract

Primary hypertrophic osteoarthropathy or pachydermoperiostosis is a rare hereditary disorder characterized by digital clubbing, pachydermia and periostosis. Its precise incidence and prevalence is still unknown due to the lack of controlled data. It occurs without any underlying causes and usually has a chronic course. Life expectancy may be of normal standards, but many patients develop multiple functional and cosmetic complications. So, it is important to diagnose this disease at an early stage and to treat the symptomat for the quality of life. We report a case of primary hypertrophic osteoarthropathy in a 68-year-old male with clinical features such as digital clubbing and pachydermia, radiographic findings of acroosteolysis and periosteal new bone formation.