Journal of the Korean Radiological Society  1992;28(1):101-103

doi:10.3348/jkrs.1992.28.1.101

Primary pulmonary histiocytosis X: a case report.

Ki Yeol LEE ; Eun Young KANG ; Kyoo Byung CHUNG ; Yang Seok CHAE ; Hark Jei KIM

Country

Republic of Korea

Language

Korean

Abstract

Pulmonary histiocytosis X is a rare granulomatous disorder of unknown etiology that alters the interstitium of the lung. When confined to the lung, it is known as primary pulmonary histiocytosis X or eosinophilic granuloma of the lung. The chest radiograph shows characteristic nodular, reticular, and cystic abnormalities, which are most apparent in the upper and middle lung zones, but spare the costophrenic angles, The CT demonstrates innumerable small cysts with thin walls, and fine nodules. Recently we experienced pathologically proven primary pulmonary histiocystosis X in 35 years old male patients who had recurrent pneumothorax.