Clinical and Experimental Otorhinolaryngology  2008;1(4):224-226

Juvenile Paget's Disease with Paranasal Sinus Aplasia.

Ki Beom BAE 1 ; Jae Hwan KWON ; Young Ho KIM ; Tae Young JUNG ; Joong Hwan CHO

Affiliations

+expand

Keywords

Paget disease of bone; Osteitis deformans; Paranasal sinuses; Paranasal sinus neoplasms

Country

Republic of Korea

Language

English

Abstract

Juvenile Paget's disease (JPD) is a rare skeletal disorder that's characterized by bone demineralization and elevated levels of serum alkaline phosphatase. JPD involves the paranasal sinuses in extremely rare cases. We report here on a 25-month-old Asian male who was diagnosed of JPD associated with aplasia of the paranasal sinuses, but not the ethmoid sinuses. The patient was successfully treated by surgery and we undertook no medical intervention. This appears to be the first reported case of JPD associated with bilateral paranasal sinus aplasia.