Korean Journal of Perinatology  2014;25(4):307-310

doi:10.14734/kjp.2014.25.4.307

Glial Choristoma Accompanied with Severe Bony Defect in Orbit in a Newborn.

Suk Hwan HAN 1 ; Tae Hee KIM ; Na Mi LEE ; Jae Kyun KIM ; She Young LEE

Affiliations

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Keywords

Brain; Choristoma; Heterotopia; Orbit; Newborn

Country

Republic of Korea

Language

Korean

Abstract

Glial choristoma is a mass-like lesion composed of otherwise normal, mature brain tissue that is isolated from the spinal cord and cranial cavity. In generally, this choristoma involves extracranial midline structures, especially the nose, as well as the nasopharynx, oropharynx and cleft. Glial choristomas rarely involve extracranial non-midline structures such as the scalp, orbit, middle ear or mastoid and account for approximately 10% of all glial choristomas. Moreover, such glial choristoma presentations are usually seen in adults, most of whom have predisposing factors such as trauma, surgery, or chronic inflammation. Here, we present a case of a glial choristoma that invaded a neonate's the nasopharynx, oropharynx, oral cavity and orbit.