Journal of the Korean Society for Vascular Surgery  2001;17(2):291-298

Treatment of Budd-Chiari Syndrome by Porto-cavo-atrial Bypass: A case report.

Woo Jin KIM 1 ; Ji Il KIM ; Sun Cheol PARK ; In Sung MOON ; Jang Sang PARK ; Seung Nam KIM ; Yong Bok KOH

Affiliations

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Keywords

Budd-chiari syndrome; Porto-cavo-atrial

Country

Republic of Korea

Language

Korean

Abstract

Budd-Chiari Syndrome (BCS) is unusual form of portal hypertension caused by occlusion of the hepatic venous outflow and it is often frequently complicated by inferior vena cava (IVC) occlusion. It may vary in its presentation from very mild symptomatology, suggestive of a viral illness, to a very acute form with a fulminant course. In the cases of BCS caused by occlusion of IVC and hepatic vein, none of the standard portal-systemic shunt can be utilized for satisfactory decompression of the liver. We have experienced two cases of BCS, 43 year-old male and 40 year-old male patients, caused by hepatic vein thrombosis associated thrombosis of the IVC. Cavoatrial shunt using Dacron graft and interposition graft between portal vein to cavoatrial graft were performed. Combined porto-cavo-atrial bypass that decompress both the portal system and IVC has been effective in relieving BCS caused by occlusion of hepatic vein with IVC.