Chinese Journal of Inflammatory Bowel Diseases 2020;04(2):168-170

doi:10.3760/cma.j.cn101480-20190605-00082

A case of Degos disease with intestinal microperforation

Weiwei ZHENG 1 ; Mi WANG ; Yijuan LIN ; Xunru HUANG ; Zehao ZHUANG ; Chengdang WANG

Affiliations

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Keywords

Degos disease; Malignant atrophic papulosis; Intestinal perforation; Micro

Country

China

Language

Chinese

Abstract

Degos disease is a rare multi-system necrotic vasculitis disease. Autoimmune abnormality, heredity, infection and coagulation abnormality may be involved in the disease. Usually skin manifestations would be the first manifestation of this disease. However, intestinal perforation and hemorrhage are the main causes of death, which are not easy to be recognized or diagnosed by gastroenterologist. A case of this rare disease with intestinal microperforation is reported for reference.